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N-Isovalerylglycine
CAS No. 16284-60-9
N-Isovalerylglycine ( N-Isovaleroylglycine | Isovaleroylglycine )
产品货号. M19997 CAS No. 16284-60-9
异戊酰甘氨酸 (IVG) 是一种酰基甘氨酸。酰基甘氨酸通常是脂肪酸的次要代谢物。然而,某些酰基甘氨酸的排泄在一些先天性代谢缺陷中会增加。在某些情况下,体液中这些代谢物的测量可用于诊断与线粒体脂肪酸β-氧化相关的疾病。
纯度: >98% (HPLC)
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规格 | 价格/人民币 | 库存 | 数量 |
5MG | ¥543 | 有现货 |
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10MG | ¥794 | 有现货 |
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50MG | ¥1750 | 有现货 |
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100MG | 获取报价 | 有现货 |
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200MG | 获取报价 | 有现货 |
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500MG | 获取报价 | 有现货 |
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1G | 获取报价 | 有现货 |
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生物学信息
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产品名称N-Isovalerylglycine
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注意事项本公司产品仅用于科研实验,不得用于人体或动物的临床与诊断
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产品简述异戊酰甘氨酸 (IVG) 是一种酰基甘氨酸。酰基甘氨酸通常是脂肪酸的次要代谢物。然而,某些酰基甘氨酸的排泄在一些先天性代谢缺陷中会增加。在某些情况下,体液中这些代谢物的测量可用于诊断与线粒体脂肪酸β-氧化相关的疾病。
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产品描述Isovalerylglycine (IVG) is an acyl glycine. Acyl glycines are normally minor metabolites of fatty acids. However the excretion of certain acyl glycines is increased in several inborn errors of metabolism. In certain cases the measurement of these metabolites in body fluids can be used to diagnose disorders associated with mitochondrial fatty acid beta-oxidation. Acyl glycines are produced through the action of glycine N-acyltransferase which is an enzyme that catalyzes the chemical reaction: acyl-CoA + glycine < -- > CoA + N-acylglycine. Isovalerylglycine is a byproduct of the catabolism of the amino acid leucine. Accumulation of isovalerylglycine occurs in Isovaleric Acidemia (IVA).
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体外实验——
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体内实验——
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同义词N-Isovaleroylglycine | Isovaleroylglycine
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通路Others
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靶点Other Targets
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受体Others
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研究领域——
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适应症——
化学信息
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CAS Number16284-60-9
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分子量159.18
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分子式C7H13NO3
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纯度>98% (HPLC)
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溶解度DMSO: 5 mg/mL;Methanol: 2 mg/mL
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SMILESCC(C)CC(=O)NCC(O)=O
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化学全称——
运输与储存
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储存条件(-20℃)
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运输条件With Ice Pack
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稳定性≥ 2 years
参考文献
1.Shigematsu Y et al. Stable-isotope dilution measurement of isovalerylglycine by tandem mass spectrometry in newborn screening for isovaleric acidemia. Clin Chim Acta. 2007 Nov-Dec;386(1-2):82-6.