L-allo-Isoleucine

本公司产品仅用于科研实验，不得用于人体或动物的临床与诊断

L-别异亮氨酸是一种支链氨基酸，是L-异亮氨酸的立体异构体。它是人体血浆的常见成分（尽管含量较低）。 L-别异亮氨酸是异亮氨酸转氨作用的副产物。血浆L-别异亮氨酸源自体内L-异亮氨酸，可用于诊断枫糖浆尿病（MSUD），一种遗传性疾病。

L-alloisoleucine is a branched chain amino acid and is a stereoisomer of L-isoleucine. It is a common constituent of human plasma (albeit at low levels). L-alloisoleucine is produced as a byproduct of isoleucine transamination. Plasma L-alloisoleucine which is derived from L-isoleucine in vivo can be used for the diagnosis of maple syrup urine disease (MSUD) a genetic disorder. Indeed plasma L-alloisoleucine levels above 5 μmol/L is the most specific and most sensitive diagnostic marker for all forms of MSUD.

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(3R)-LS-Isoleucine | L(+)-Alloisoleucine

Others

Other Targets

Others

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1509-34-8

131.17

C6H13NO2

>98% (HPLC)

DMSO:10 mM

CC[C@@H](C)[C@H](N)C(O)=O

(2S3R)-2-Amino-3-methylpentanoic acid

(-20℃)

With Ice Pack

≥ 2 years